Haddad syndrome ȯ¾ÆÀÇ Àü½Å¸¶Ãë ÇÏ Ä¡¾Æ¿ì½Ä Ä¡·á - Áõ·Êº¸°í
DENTAL TREATMENT OF A PATIENT WITH HADDAD SYNDROME UNDER GENERAL ANESTHESIA - CASE REPORT -
¼Èñ¿ø, ¼ÛÁö¼ö, ½ÅÅÍÀü, ÇöÈ«±Ù, ±è¿µÀç, ±èÁ¤¿í, ÀÌ»óÈÆ, Àå±âÅÃ,
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¼Èñ¿ø ( Suh Hee-Won ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
¼ÛÁö¼ö ( Song Ji-Soo ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
½ÅÅÍÀü ( Shin Teo-Jeon ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
ÇöÈ«±Ù ( Hyun Hong-Keun ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
±è¿µÀç ( Kim Young-Jae ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
±èÁ¤¿í ( Kim Jung-Wook ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
ÀÌ»óÈÆ ( Lee Sang-Hoon ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
Àå±âÅà ( Jang Ki-Taeg ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
KMID : 1144020170130010047
Abstract
Haddad syndrome, the association of Congenital Central Hypoventilation Syndrome (CCHS) and Hirschsprung¡¯s disease (HD), is a disease caused by mutation of PHOX2B gene. This disease, which occurs very rarely worldwide, is characterized by adequate ventilation during wakefulness and hypoventilation during sleep due to decreased ventilatory sensitivity. In this case report, we report a case of dental treatment under general anesthesia in a child with Haddad syndrome.
A 3-year-old child with Haddad syndrome visited Seoul National University Dental Hospital for dental treatment. Dental treatment was planned under general anesthesia because of his medical condition. Treatment was successfully done without any postoperative complications. This case suggests that general anesthesia may be advantageous for dental treatment due to the risk of respiratory depression in a child with Haddad syndrome.
Å°¿öµå
Haddad syndrome; Congenital Central hypoventilation syndrome; Hirschsprung¡¯s disease; Dental treatment; General anesthesia
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